Mastocytosis with clinical features of histyocitosis.
How to Cite
Betto P., Gennari E., Cambiaghi S., Niccoli A. 2006. Mastocytosis with clinical features of histyocitosis. Eur. J. Pediat. Dermatol. 16 (2): 95.
AbstractCutaneous mastocytosis is a rare disorder characterized by an increased number of mastocytes in the dermis. Pseudoxanthomatous mastocytosis is a rare clinical variant reported by Fox in 1883, clinically characterized by yellowish and brownish papules and nodules, wich are reminiscent of xanthoma or histiocytosis. The Darier sign is slightly positive.