TY - JOUR AU - Despontin, K. AU - Bottu, J. AU - Decroix, J. AU - Otte, J.B. AU - Lachapelle, J.M. PY - 2018/06/24 Y2 - 2024/03/29 TI - Syndromic paucity of interlobular bile ducts or Alagille syndrome: a case report. JF - European Journal of Pediatric Dermatology JA - Eur. J. Pediat. Dermatol. VL - 1 IS - 1 SE - DO - UR - https://www.ejpd.com/index.php/journal/article/view/1829 SP - 35-39 AB - <p>A case of syndromic paucity of interlobular bile ducts (Alagille syndrome) is report­ed in an 8-year-old child. Chronic intrahepatic cholestasis is described in association with vertebral, cardio­vascular, ophthalmogical and renal abnormalities. Various skin manifestations includ­ing xanthomas, jaundice and pruritus are present secondary to biliary and liver failure.</p> ER -